{"id":3300,"date":"2018-10-27T16:18:21","date_gmt":"2018-10-27T13:18:21","guid":{"rendered":"https:\/\/blog.annebebekkulubu.com\/?p=3300"},"modified":"2018-10-27T16:18:21","modified_gmt":"2018-10-27T13:18:21","slug":"kacis-sendromu-hastaligi-nedir-belirtileri-nelerdir","status":"publish","type":"post","link":"https:\/\/annebebekkulubu.com\/blog\/kacis-sendromu-hastaligi-nedir-belirtileri-nelerdir\/","title":{"rendered":"Ka\u00e7\u0131\u015f sendromu hastal\u0131\u011f\u0131 nedir? Belirtileri nelerdir?"},"content":{"rendered":"<p>Halk aras\u0131nda \u201cKa\u00e7\u0131\u015f Sendromu\u201d olarak bilinen \u201cSistemik Kapiller<strong> Ka\u00e7\u0131\u015f Sendromu<\/strong>\u201d; olu\u015fum mekanizmas\u0131, belirtileri ve seyri a\u00e7\u0131s\u0131ndan ilgin\u00e7 ve farkl\u0131 bir hastal\u0131kt\u0131r. G\u00fcndelik hayat s\u0131ras\u0131nda ve normal \u015fartlarda herhangi bir belirti vermeyen ancak ataklar s\u0131ras\u0131nda ciddi \u015fikayetler ile seyreden bu hastal\u0131k yeterli ve gerekli tedaviler uygulanmaz ise \u00f6l\u00fcmc\u00fcl seyreder.<\/p>\n<p><strong>Nadir g\u00f6r\u00fclen bir hastalik<\/strong><\/p>\n<p>Literat\u00fcrde tan\u0131mlanm\u0131\u015f hasta say\u0131s\u0131 1000in alt\u0131nda olan bu hastal\u0131k her iki cinsiyette de yakla\u015f\u0131k olarak e\u015fit oranda g\u00f6r\u00fcl\u00fcr (E %57, K %43). Literat\u00fcr bilgilerine g\u00f6re tan\u0131mlanm\u0131\u015f ortalama hasta ya\u015f\u0131 47 olmakla birlikte hastal\u0131\u011f\u0131n g\u00f6r\u00fcld\u00fc\u011f\u00fc en k\u00fc\u00e7\u00fck hasta 5 ayl\u0131k bir \u00e7ocuk iken en ya\u015fl\u0131 hasta ise 74 ya\u015f\u0131ndad\u0131r.<\/p>\n<p><strong>Ka\u00e7\u0131\u015f sendromu hastal\u0131\u011f\u0131n\u0131n belirtileri nelerdir?\u00a0<\/strong><\/p>\n<p>Normal \u015fartlarda herhangi bir sorunu olmayan ki\u015filerde, ataklar halinde seyreden bu hastal\u0131kta en belirgin \u00f6zellik, v\u00fccuttaki k\u0131lcal damarlarda ge\u00e7irgenli\u011fin artmas\u0131 ve buna ba\u011fl\u0131 olarak kan\u0131n s\u0131v\u0131 k\u0131sm\u0131n\u0131n ve makromolek\u00fcllerin baz\u0131lar\u0131n\u0131n damar d\u0131\u015f\u0131na s\u0131zmas\u0131d\u0131r. K\u0131lcal damarlarda bu ani sorunu yaratan mekanizman\u0131n ne oldu\u011fu hen\u00fcz tam olarak ortaya konamam\u0131\u015ft\u0131r ancak imm\u00fcn sistemde yani v\u00fccudun savunma sistemindeki bir bozuklu\u011fun bu duruma sebep oldu\u011fu d\u00fc\u015f\u00fcn\u00fclmektedir. Damar d\u0131\u015f\u0131na s\u0131v\u0131 s\u0131zmas\u0131 hem damar i\u00e7indeki kan miktar\u0131n\u0131n azalmas\u0131na hem de g\u00f6\u011f\u00fcs, kar\u0131n, kalp zar\u0131 gibi v\u00fccut bo\u015fluklar\u0131nda s\u0131v\u0131 birikmesine neden olmaktad\u0131r. Bununla birlikte yayg\u0131n \u00f6dem olu\u015fumu da s\u00f6z konusudur. Bu s\u0131v\u0131 da\u011f\u0131l\u0131m\u0131ndaki ani ve sa\u011fl\u0131ks\u0131z de\u011fi\u015fim elektrolit seviyelerinin de bozulmas\u0131na neden olur.<\/p>\n<p>T\u00fcm bu de\u011fi\u015fiklikler<strong> ani tansiyon d\u00fc\u015fmesi, halsizlik, bulant\u0131, kusma, t\u00fcm v\u00fccutta \u015fi\u015flik<\/strong> gibi \u00e7ok tan\u0131mlay\u0131c\u0131 olmayan genel baz\u0131 \u015fikayetlere sebep olurlar. Bununla birlikte <strong>kalp zar\u0131nda ve g\u00f6\u011f\u00fcs bo\u015flu\u011funda s\u0131v\u0131 birikmesi durumunda akci\u011fer ve kalp yetersizli\u011fi g\u00f6r\u00fclebilir ve hayat\u0131 tehdit edici durumlar ortaya \u00e7\u0131kabilir.<\/strong><\/p>\n<p>Nedeni, mekanizmas\u0131 tam olarak \u00e7\u00f6z\u00fclememi\u015f bu hastal\u0131k en \u00e7ok enfeksiyonlara ba\u011fl\u0131 geli\u015fen \u201c<strong>septik \u015fok<\/strong>\u201d ile kar\u0131\u015ft\u0131r\u0131l\u0131r. Bunun yan\u0131nda a\u015f\u0131r\u0131 alerjik reaksiyon olarak tan\u0131mlanabilecek anaflaktik \u015fok, akut b\u00f6brek yetmezli\u011fi yaratabilecek baz\u0131 tablolar da \u201cKa\u00e7\u0131\u015f Sendromu\u201d ile kar\u0131\u015ft\u0131r\u0131labilir. Herhangi bir \u015fekilde tan\u0131 koydurtacak \u00f6zel bir laboratuvar testi bulunmamakla birlikte kan\u0131n normalden daha koyu hale gelmesi (hemokonsantrasyon), bir kan proteini olan alb\u00fcmin de\u011ferlerinde d\u00fc\u015f\u00fckl\u00fck, sodyum ve potasyum dengesizlikleri gibi bulgular varl\u0131\u011f\u0131nda \u201c<strong>Ka\u00e7\u0131\u015f Sendromu\u201d<\/strong>ndan \u015f\u00fcphelenmek gereklidir.<\/p>\n<p><strong>Ka\u00e7\u0131\u015f sendromu hastal\u0131\u011f\u0131 nasil tedavi edilir?\u00a0<\/strong><\/p>\n<p>Tedavide as\u0131l ama\u00e7 ataklar s\u0131ras\u0131nda tansiyon d\u00fc\u015f\u00fckl\u00fc\u011f\u00fcn\u00fc engellemek, kan\u0131n miktar\u0131n\u0131 yeterli seviyede tutmak, s\u0131v\u0131 ve elektrolit dengesini korumak ve bu sayede kalp-beyin-b\u00f6brek gibi hayati organlar\u0131n beslenmesinin devaml\u0131l\u0131\u011f\u0131n\u0131 sa\u011flamakt\u0131r. Bununla birlikte bozulmu\u015f organ fonsiyonlar\u0131 i\u00e7inde ivedi bir \u015fekilde tan\u0131 koymak ve bu y\u00f6nde gerekli giri\u015fimleri yapmak hayat kayb\u0131n\u0131 \u00f6nlemek a\u00e7\u0131s\u0131ndan \u00f6nem ta\u015f\u0131r. Ataklar aras\u0131nda ise ast\u0131m tedavisinde de kullan\u0131lan baz\u0131 ila\u00e7lar, steroid (kortizol) tedavisi ve imm\u00fcn sistemi d\u00fczenleyen di\u011fer baz\u0131 tedavi y\u00f6ntemleri de kullan\u0131labilmektedir.<\/p>\n<p>Sa\u011fl\u0131kl\u0131 haftalar dilerim.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Halk aras\u0131nda \u201cKa\u00e7\u0131\u015f Sendromu\u201d olarak bilinen \u201cSistemik Kapiller Ka\u00e7\u0131\u015f Sendromu\u201d; olu\u015fum mekanizmas\u0131, belirtileri ve seyri a\u00e7\u0131s\u0131ndan ilgin\u00e7 ve farkl\u0131 bir hastal\u0131kt\u0131r. G\u00fcndelik hayat s\u0131ras\u0131nda ve normal \u015fartlarda herhangi bir belirti vermeyen ancak ataklar s\u0131ras\u0131nda ciddi \u015fikayetler ile seyreden bu hastal\u0131k yeterli ve gerekli tedaviler uygulanmaz ise \u00f6l\u00fcmc\u00fcl seyreder. Nadir g\u00f6r\u00fclen bir hastalik Literat\u00fcrde tan\u0131mlanm\u0131\u015f hasta [&hellip;]<\/p>\n","protected":false},"author":16,"featured_media":3009,"comment_status":"open","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"jetpack_post_was_ever_published":false,"_jetpack_newsletter_access":"","_jetpack_dont_email_post_to_subs":false,"_jetpack_newsletter_tier_id":0,"_jetpack_memberships_contains_paywalled_content":false,"_jetpack_memberships_contains_paid_content":false,"footnotes":""},"categories":[7],"tags":[2643,2642,2646,2645,2644],"class_list":["post-3300","post","type-post","status-publish","format-standard","has-post-thumbnail","category-saglik","tag-kacis-hastaligi","tag-kacis-sendromu-hastaligi","tag-kacis-sendromu-hastaligi-belirtileri","tag-kacis-sendromu-tedavisi","tag-mehmet-ali-erbilin-hastaligi"],"jetpack_sharing_enabled":true,"jetpack_featured_media_url":"https:\/\/i0.wp.com\/annebebekkulubu.com\/blog\/wp-content\/uploads\/2018\/08\/mutsuz-kadin.jpg?fit=1000%2C664&ssl=1","jetpack-related-posts":[],"_links":{"self":[{"href":"https:\/\/annebebekkulubu.com\/blog\/wp-json\/wp\/v2\/posts\/3300","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/annebebekkulubu.com\/blog\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/annebebekkulubu.com\/blog\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/annebebekkulubu.com\/blog\/wp-json\/wp\/v2\/users\/16"}],"replies":[{"embeddable":true,"href":"https:\/\/annebebekkulubu.com\/blog\/wp-json\/wp\/v2\/comments?post=3300"}],"version-history":[{"count":0,"href":"https:\/\/annebebekkulubu.com\/blog\/wp-json\/wp\/v2\/posts\/3300\/revisions"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/annebebekkulubu.com\/blog\/wp-json\/wp\/v2\/media\/3009"}],"wp:attachment":[{"href":"https:\/\/annebebekkulubu.com\/blog\/wp-json\/wp\/v2\/media?parent=3300"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/annebebekkulubu.com\/blog\/wp-json\/wp\/v2\/categories?post=3300"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/annebebekkulubu.com\/blog\/wp-json\/wp\/v2\/tags?post=3300"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}